maple syrup disease

     

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  • RT @UsmleAid: Maple Syrup Disease: α Ketoacid Dehydrogenase deficiency. Rx: Avoid Branched Chain Amino Acids viz. Isoleucine, Leucine & Val…
  • Maple Syrup Disease: α Ketoacid Dehydrogenase deficiency. Rx: Avoid Branched Chain Amino Acids viz. Isoleucine, Leucine & Valine. #MedEd